Research
Tag

Urea Cycle

5 genetic variants with this tag.

RSID Gene Description Category
rs146582474 SLC7A7 Finnish founder splice acceptor mutation abolishing y+LAT1 transport activity... Metabolic Enzymes & Rare Disorders Established
rs28933978 OTC R141Q (Arg141Gln) The most common OTC point mutation, abolishing ornithine transcarbamylase enz... Metabolic Enzymes & Rare Disorders Established
rs367543005 ASL p.Gln354Ter (Q354X) Nonsense mutation in argininosuccinate lyase introducing a premature stop cod... Metabolic Enzymes & Rare Disorders Established
rs72552272 SLC7A7 L334R Pathogenic missense in the y+LAT1 cationic amino acid transporter causing lys... Metabolic Enzymes & Rare Disorders Established
rs72552297 OTC Asn10fs (c.29_32del) Frameshift deletion in the OTC gene that eliminates ornithine transcarbamylas... Metabolic Enzymes & Rare Disorders Established