Research
Tag

Hearing Loss

18 genetic variants with this tag.

RSID Gene Description Category
rs104894396 GJB2 W24X Stop-gain mutation eliminating connexin 26 function; the most common GJB2 dea... Neurology & Cognition Established
rs10514168 TSHZ1 Intergenic variant downstream of TSHZ1, a transcription factor essential for ... Neurology & Cognition Strong
rs137853096 HSD17B4 Gly16Ser Pathogenic missense variant in D-bifunctional protein (p.Gly16Ser) disrupting... Metabolic Enzymes & Rare Disorders Established
rs1978060 TBX1 Intronic variant in TBX1 acting as a cis-eQTL that reduces TBX1 expression an... Innate Immunity & Infection Defense Moderate
rs137853097 HSD17B4 N457Y Missense variant in the enoyl-CoA hydratase domain of D-bifunctional protein;... Metabolic Enzymes & Rare Disorders Established
rs2251780 GSR Intronic variant in the glutathione reductase gene affecting antioxidant defe... Vitamins & Nutrient Absorption Emerging
rs2531693353 HSD17B4 c.715-1G>A (splice acceptor) Rare splice acceptor variant disrupting intron 9 of D-bifunctional protein; b... Metabolic Enzymes & Rare Disorders Established
rs137853000 TMPRSS3 p.Arg216Leu (R216L) Pathogenic missense variant at the TMPRSS3 autocatalytic cleavage site causin... Neurology & Cognition Strong
rs397514538 SLC52A2 Pathogenic missense variant in riboflavin transporter RFVT2 (p.Leu123Pro) cau... Vitamins & Nutrient Absorption Established
rs181949335 TMPRSS3 p.Ala306Thr (A306T) Hypomorphic missense variant in the TMPRSS3 serine protease catalytic domain;... Neurology & Cognition Strong
rs73015965 PLG Lys38Glu (K38E) Missense variant in plasminogen that reduces fibrinolytic activity and impair... Innate Immunity & Infection Defense Strong
rs35887622 GJB2 M34T Connexin 26 missense variant causing partial loss of cochlear gap junction fu... Neurology & Cognition Established
rs45598239 TMPRSS3 Near-gene variant tagging the TMPRSS3 hearing loss locus on chromosome 21, as... Neurology & Cognition Moderate
rs72474224 GJB2 V37I Connexin 26 missense variant causing partial loss of cochlear gap junction fu... Neurology & Cognition Established
rs727503493 TMPRSS3 c.208delC (p.His70Thrfs*19) Frameshift deletion in TMPRSS3 causing premature stop at codon 88; a severe p... Neurology & Cognition Strong
rs80338939 GJB2 35delG The most common cause of autosomal recessive nonsyndromic hearing loss in Eur... Neurology & Cognition Established
rs80338942 GJB2 167delT The most common GJB2 deafness allele in the Ashkenazi Jewish population (~4% ... Neurology & Cognition Established
rs80338943 GJB2 c.235delC Frameshift deletion eliminating connexin 26 function; the most common GJB2 de... Neurology & Cognition Established